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hypocomplementemic urticarial vasculitis

Disease Summary
Associated Targets (1)
Tbio

1


GARD Rare
Mondo Description Hypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usually associated with circulating anti-C1q autoantibodies. Arthritis, pulmonary disease, ocular inflammation, and glomerulonephritis are common systemic manifestations.
Mondo Term and Equivalent IDs
MONDO:0018227:  hypocomplementemic urticarial vasculitis
GARD:0006725: 
Orphanet:36412: 
SCTID:239945009: 
UMLS:C0343206: 
UMLS:CN204757: