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diffuse cutaneous systemic sclerosis

Disease Summary
Associated Targets (17)
Tbio

9

Tdark

6

Tchem

2


GARD Rare
Mondo Description Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc) characterized by truncal and acral skin fibrosis with an early and significant incidence of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse gastrointestinal disease, and myocardial involvement).
Mondo Term and Equivalent IDs
MONDO:0016356:  diffuse cutaneous systemic sclerosis
GARD:0009751: 
NCIT:C116791: 
Orphanet:220393: