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idiopathic pulmonary arterial hypertension

Disease Summary
Associated Targets (20)
Tbio

11

Tclin

5

Tchem

4


Mondo Description Idiopathic pulmonary arterial hypertension (IPAH) is a sporadic form of pulmonary arterial hypertension (PAH) characterized by elevated pulmonary arterial resistance leading to right heart failure. IPAH is progressive and potentially fatal and not associated with an underlying condition or family history of PAH.
Mondo Term and Equivalent IDs
MONDO:0017147:  idiopathic pulmonary arterial hypertension
ICD9:416.0: 
Orphanet:275766: 
SCTID:697898008: 
UMLS:C3203102: 
UMLS:CN202574: