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primary progressive aphasia

Disease Summary
Associated Targets (8)
Tbio

5

Tchem

2

Tclin

1


GARD Rare
Mondo Description Primary progressive aphasia (PPA) is a neurodegenerative disorder, characterized by a primary dissolution of language, with relative sparing of other mental faculties for at least the first 2 years of illness. PPA is recognized as the language variant in the frontotemporal dementia (FTD) spectrum of disorders. PPA can be classified into 3 subtypes based on specific speech and language features: semantic dementia (SD), progressive non-fluent aphasia (PNFA) and logopenic progressive aphasia (lv-PPA).
Mondo Term and Equivalent IDs
MONDO:0019806:  primary progressive aphasia
EFO:0009053: 
GARD:0008541: 
MESH:D018888: 
NCIT:C85024: 
Orphanet:95432: 
UMLS:C0282513: