Disease Summary help help Associated Targets (1)Tbio1 Explore Associated Targets list GARD Rare open_in_new Mondo Description Otodental syndrome is a very rare inherited condition characterized by grossly enlarged canine and molar teeth (globodontia) associated with sensorineural hearing loss. Mondo Term and Equivalent IDs MONDO:0008161: otodental syndrome GARD:0004168: open_in_newOMIM:166750: OTODENTAL DYSPLASIAopen_in_newOrphanet:2791: SCTID:707310009: open_in_newUMLS:C1833693: open_in_new