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choroid plexus papilloma

Disease Summary
Associated Targets (1)
Tchem

1


GARD Rare
Mondo Description Papilloma of the choroid plexus is a rare benign type of choroid plexus tumor, accounting for 1% of all brain tumors, often occurring in the fourth ventricle (in adults) and the lateral ventricle (in children) but sometimes arising ectopically in the brain parenchyma, and presenting with nausea, vomiting, papilledema, abnormal eye movements, as well as enlarged head circumference, seizures and gait impairment due to an increase in intracranial pressure.
Uniprot Description A benign tumor of neuroectodermal origin that generally occurs in childhood, but has also been reported in adults. Although generally found within the ventricular system, choroid plexus papillomas can arise ectopically in the brain parenchyma or disseminate throughout the neuraxis. Patients present with signs and symptoms of increased intracranial pressure including headache, hydrocephalus, papilledema, nausea, vomiting, cranial nerve deficits, gait impairment, and seizures.
Mondo Term and Equivalent IDs
MONDO:0009837:  choroid plexus papilloma
EFO:1000177: 
GARD:0004214: 
MESH:D020288: 
NCIT:C3698: 
ONCOTREE:CPP: 
Orphanet:2807: 
SCTID:425868004: 
UMLS:C0205770: