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frontotemporal dementia with motor neuron disease
Disease Summary
Associated Targets (8)
Tbio
5
Tchem
3
Mondo Description Frontotemporal dementia with motor neuron disease (FTD-MND) is a type of frontotemporal lobar degeneration characterized by the insidious onset (between the ages of 38-78 years) of dementia-associated psychiatric symptoms (e.g. personality changes, uninhibited behavior, irritability, aggressiveness), memory difficulties, global intellectual impairment, emotional disorders and transcortical motor aphasia that eventually leads to mutism, in addition to the manifestations of motor neuron disease such as neurogenic muscular wasting (similar to what is seen in amyotrophic lateral sclerosis). The disease is progressive, with death occurring 2-5 years after onset.
Mondo Term and Equivalent IDs
MONDO:0017161: frontotemporal dementia with motor neuron disease
Download Data for frontotemporal dementia with motor neuron disease
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Counts of Target Development Levels for diseases known to be associated with this disease. If the disease has a valid DOID, targets known to be associated with all child diseases are aggregated. Click "Explore Associated Targets" to view more facets and details for the target list.
Description from Mondo Disease Ontology.
DataSources which have contributed target associations to this disease, and the identifiers by which the disease is referenced.
OMIMPS:105550
Orphanet:275872
UMLS:C3888102
UMLS:CN239493
MONDO:0017161
High level summary of knowledge for a disease, including descriptions and datasource references.