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papillary ependymoma

Disease Summary
Associated Targets (6)
Tbio

3

Tdark

2

Tchem

1


Mondo Description A rare variant of ependymoma characterized by well formed papillae. Tumor cell processes abutting capillaries are usually GFAP-positive. Differential diagnoses include choroid plexus papilloma, papillary meningioma and metastatic papillary carcinoma. (Adapted from WHO)
Mondo Term and Equivalent IDs
MONDO:0003475:  papillary ependymoma
NCIT:C4319: 
UMLS:C0334578: