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primitive neuroectodermal tumor of the cervix uteri

Disease Summary
Associated Targets ()

Mondo Description Primitive neuroectodermal tumor of the cervix uteri is a rare cancer of cervix uteri derived from neural crest cells, histologically composed of small, round neoplatic cells with variable degree of neural, glial and ependymal differentiation. Macroscopically, the tumor is often a large, soft, poorly circumscribed mass with infiltrative borders and necrotic areas. It presents with dysfuntional vaginal bleeding or discharge, lower abdominal pain and uterine enlargement.
Mondo Term and Equivalent IDs
MONDO:0016284:  primitive neuroectodermal tumor of the cervix uteri
Orphanet:213812: 
UMLS:CN201074: