Disease Summary help help Associated Targets (1)Tchem1 Explore Associated Targets list GARD Rare open_in_new Mondo Description Phakomatosis pigmentokeratotica (PPK) is a very rare epidermal nevus disorder characterized by the association of speckled lentiginous nevi with epidermal sebaceous nevi, and extracutaneous anomalies. Mondo Term and Equivalent IDs MONDO:0017317: phakomatosis pigmentokeratotica GARD:0004311: open_in_newMESH:C537893: open_in_newOrphanet:2874: SCTID:723455009: open_in_newUMLS:C2931658: open_in_new