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hereditary pheochromocytoma-paraganglioma

Disease Summary
Associated Targets (31)
Tclin

14

Tbio

13

Tchem

4


Mondo Description Hereditary paraganglioma-pheochromocytomas (PGL/PCC) are rare neuroendocrine tumors represented by paragangliomas (occurring in any paraganglia from the skull base to the pelvic floor) and pheochromocytomas (adrenal medullary paragangliomas).
Mondo Term and Equivalent IDs
MONDO:0017366:  hereditary pheochromocytoma-paraganglioma
GARD:0011984: 
Orphanet:29072: 
UMLS:C1708353: