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dermatofibrosarcoma protuberans

Disease Summary
Associated Targets (13)
Tchem

7

Tclin

3

Tbio

3


GARD Rare
Mondo Description Dermatofibrosarcoma protuberans (DFSP) is a rare infiltrating soft tissue sarcoma, generally of low grade malignancy, arising from the dermis of the skin and characteristically associated with a specific chromosomal translocation t(17;22).
Disease Ontology Description A fibrosarcoma that is located_in the dermis laryer of the skin and that begins as a hard nodule and grows slowly.
Mondo Term and Equivalent IDs
MONDO:0011934:  dermatofibrosarcoma protuberans
GARD:0009569: 
MESH:D018223: 
NCIT:C4683: 
ONCOTREE:DFSP: 
Orphanet:31112: 
SCTID:276799004: 
UMLS:C0392784: