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dedifferentiated chondrosarcoma

Disease Summary
Associated Targets ()

Mondo Description An aggressive morphologic variant of chondrosarcoma. It is composed of a low grade chondrosarcoma and a high grade non-cartilagenous sarcomatous component. Due to the aggressive nature of the disease, its prognosis is poor.
Mondo Term and Equivalent IDs
MONDO:0005013:  dedifferentiated chondrosarcoma
EFO:0000394: 
NCIT:C6476: 
ONCOTREE:DDCHS: 
UMLS:C0862878: