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Ewing sarcoma/peripheral primitive neuroectodermal tumor

Disease Summary
Associated Targets (32)
Tbio

23

Tchem

6

Tclin

2

Tdark

1


Mondo Description A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.
Mondo Term and Equivalent IDs
MONDO:0021038:  Ewing sarcoma/peripheral primitive neuroectodermal tumor
NCIT:C27291: 
UMLS:C3536893: